Definition of Vestibulocochlear dysfunction progressive familial
Vestibulocochlear dysfunction progressive familial, known also as familial progressive vestibulocochlear dysfunction is an autosomal dominant disease that results in sensorineural hearing loss and vestibular areflexia. Patients report feelings of vague dizziness, blurred vision, dysequilibrium in the dark, and progressive hearing impairment.
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Frequently asked questions
What is Vestibulocochlear dysfunction progressive familial?
Vestibulocochlear dysfunction progressive familial, known also as familial progressive vestibulocochlear dysfunction is an autosomal dominant disease that results in sensorineural hearing loss and vestibular areflexia.